الفهرس 
PULMONARY HYPERTENSIONOnly 14 pages are availabe for public view
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Abstract
R
egistries of patients with pulmonary arterial hypertension (PAH) have been instrumental in characterizing the presentation and history of the disease providing a basis for prognostication. Since initial accumulation of data conducted in the 1980s, subsequent registry databases have yielded information about the demographic factors, treatment, and survival and have permitted comparisons between populations in different eras and environments. Inclusion of patients with all subtypes of PAH has also allowed comparisons of these subpopulations.
Our registry included 150 patients who were presented to the structural and congenital heart disease unit in Ain shams university hospitals, for medical treatment, catheter or surgical intervention or were following up in the cardiology department clinic starting from 1st of May 2018 till the end of May 2019.
The pediatric age group included 105 patients, 55 males (52.4%) and 50 females (47.6%).
The mean age of the group was 5 years.
All our patients were diagnosed by echocardiograph and in 81% diagnosis was confirmed by right heart catheterization.
The most common congenital anomaly was VSD then complex congenital heart disease, the most common presenting symptom was dyspnea.
The adult age group included 45 patients, 15 males (33.3%) and 30 females (66.7%).
The mean age of the group was 37 years with female predominance, the most common congenital anomaly was ASD.
The most common presenting symptom was dyspnea.
Our descriptive study confirmed many characteristic similarities between our patients, middle-east data, and the international data.
Most of our patient had pulmonary hypertension due to CHD in contrast to other registries which studied all the groups this could be justified by the specific nature of our unit which is specialized in congenital heart diseases.
There is a significant delay in treatment in Egyptian patients due to many causes as unavailability of drugs, high cost, Bureaucracy, large number of patients in the waiting lists, paucity of specialized surgeons and patient’s delay due to lack of proper health education.