الفهرس | Only 14 pages are availabe for public view |
Abstract Summary Duane syndrome (DS) is an eye movement disorder present at birth (congenital) characterized by horizontal eye movement limitation: a limited ability to move the eye inward toward the nose (adduction), outward toward the ear (abduction), or in both directions. When the affected eye(s) moves inward toward the nose, the eyeball retracts (pulls in) and the eye opening (palpebral fissure) narrows. In some patients, when the eye attempts to look inward, it moves upward (upshoot) or downward (downshoot). DRS is included in a group of disorders called congenital cranial dysinnervation disorders. These disorders can have a varied presentation which is caused by either primary or secondary dysinnervation. Type of DRS is determined by clinical examination, in which type I has limited abduction, type II has limited adduction, and type III has limited both abduction and adduction. Determination of degree of globe retraction and/or over shooting must be included to take the appropriate decision In Managing DRS, strabismus in primary position should be determined noticed, and measuring angle of deviation. Horizontal deviation in primary position is managed by unilateral or bilateral muscle recession, according to angle of deviation, degree of limitation. Simultaneous MR, LR recession, manages globe retraction with palpebral fissure narrowing. Y splitting of LR is the gold standard for treating over shooting. Conclusion DRS is a congenital strabismus disorder with the hallmark of diagnosis is limitation of movement and globe retraction. It represents 3.64% of all cases of strabismus There are specific indications that one should take in consideration in managing DRS by surgery. Treatment should be tailored to each case according to the findings and degree of each of them. Preoperative consultation is a must about the non-correctable signs. There is marked postoperative improvement in the correctable signs, and it is advised to proceed in surgery in indicated cases. |