الفهرس 
INTRODUCTIONOnly 14 pages are availabe for public view
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Abstract
Primary congenital glaucoma (PCG) is the most common non syndromic glaucoma in infancy, which can lead to blindness, or a lifetime of vision when diagnosed and treated properly.
PCG is more common in populations with a higher prevalence of consanguinity and is associated with CYP1B1 gene mutations which show variable expressivity and phenotypes.
Classic symptoms at presentation include tearing, photophobia, blepharospasm, eye rubbing, and irritability. Examination may reveal elevated intraocular pressure, corneal edema, increased corneal diameter, Haabstriae, or enlarged axial length.
Angle surgery remains the first line treatment for PCG with a recent advance being circumferential trabeculotomy with the potential to incise the whole angle during one operation as opposed to an incremental approach and the associated multiple anesthetics. Once angle surgery fails, either trabeculectomy or glaucoma drainage device surgery may be appropriate.
This study aimed to report the presenting characteristics of the children presenting with PCG to Alexandria Main University Hospital.
This study was conducted on 503 eyes of 337 children of either sex. All participants subjected to the same protocol including history and clinical ophthalmic examinationasInitial office examination was followed by an examination under general anesthesia to obtain information including:
IOP (measured using Perkins hand-held applanation tonometer), Corneal diameter (measured using catroveijo surgical caliper as horizontal white-to-white),Fundus examination (using indirect ophthalmoscope if the media clarity allowed visibility of posterior segment structures), Axial length measurement (using A-scan ultrasonography) and B-scan ultrasound if media clarity precluded clinical fundoscopy and Central Corneal Thickness measurement (using the Pachmate®, DGH technology, when this was available).