الفهرس 
Vascular supply and lymphatic drainageOnly 14 pages are availabe for public view
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Abstract
SUMMARY
Congenital adrenal hyperplasia (CAH) is the most common cause of neonatal ambiguous genitalia, most cases of virilized females with congenital adrenal hyperplasia present in the first month. The virilization degree is mostly Prader II, III and IV.
In our study, twenty cases of DSD patients were included, 18 cases had congenital adrenal hyperplasia, two cases had complete androgen insensitivity syndrome (CAIS). All cases of congenital adrenal hyperplasia had a 21-hydroxylase deficiency. 16 cases were salt wasting (SW) and 2 cases were severe simple virilizing (SV). Most of our CAH cases ranged between Prader’s IV and V degrees.
Feminizing genitoplasty is safe to be done between the age of 6 months and one year in the hands of an experienced surgical team, familiar with all alternative techniques. , most of our cases were operated before the age of 3 years with 7 cases (35%) before the age of one year. Ranging from 6 to 10 months.
The majority of cases could not be corrected by a simple flap vaginoplasty and need a degree of mobilization of the urogenital sinus. In our study the urogenital sinus mobilization was used in 17 cases (94.5%), the partial urogenital mobilization (PUM) was used in 3 cases (16.7%) and the total urogenital mobilization (TUM) was used in 14 cases (77.7%).Colon vaginoplasty was used in 3 cases two of them were complete androgen insensitivity syndrome (CAIS) and one case was congenital adrenal hyperplasia (CAH).