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Abstract There is a broad spectrum of neurogenic tumors that involve the abdomen. These tumors can be classified as being of ganglion cell origin (ganglioneuromas, ganglioneuroblastomas, neuroblastomas), paraganglionic system origin (pheochromocytomas, paragangliomas), or nerve sheath origin (neurilemmomas, neurofibromas, neurofibromatosis, malignant nerve sheath tumors). Abdominal neurogenic tumors usually follow the distribution of the sympathetic ganglia along paraspinal areas or arise from the adrenal medulla or the organ of Zuckerkandl. Occasionally, however, other sites in the abdomen such as urinary bladder, bowel wall and gallbladder can be involved. The urinary bladder is an unusual site of involvement because the trigone of the bladder contains cells of neural crest origin. The optimal treatment for abdominal neurogenic tumors is surgical removal when they are localized with no evidence of distant metastasis. Recently, laparoscopic surgery has been used. Thus, accurate preoperative localization and characterization of neurogenic tumor is important in allowing a direct surgical approach. Although all neurogenic tumors have almost similar clinical and radiologic findings, predominant or specific features are present in each type. In this essay, we describe and illustrate the clinical and imaging features of abdominal neurogenic tumors that can suggest a specific diagnosis or help substantially narrow the differential diagnosis. |